Eosinophilic Granulomatosis with Polyangitis (EGPA) and IgG4 related disease presenting as overlap Syndrome: Case report of unusual case and literature review

Abstract

EGPA is an Anti-neutrophilic Cytoplasmic antibody (ANCA ) associated vasculitis which consists of small vessel vasculitis and hypereosinophilia. There are heterogeneous presentations of EGPA, and sometimes boundaries with other hypereisophilic syndromes with respect to clinical presentation, in particular IgG4-Related disease (IgG4-D) is not clear